In 2002 the owner of HighStarr Copy Services' son, Ranger, was diagnosed with cystic fibrosis (CF) at the age of 3 months. He receives chest therapy twice a day with a pulsating chest vest, over 10 medicines per day, and takes 20 special pancreatic enzymes per day for his meals. Ranger is very accepting of all of these treatments and we have learned from his courage to take life as it comes.
CF is a life-threating genetic disease that affects the respiratory and digestive systems of tens of thousands of young children and adults. People with CF suffer from chronic, and often fatal, lung infections and have a difficulty digesting food. Ten million Americans are symptomless carriers of the defective gene which causes CF. In 1955, The CF Foundation was started by parents of children with the disease. Fifty years ago, children with CF were not expected to see their first day of elementary school. Today, more than 40 percent of the CF population is over the age of 18. Remarkable progress, but not good enough. 50% of people with CF make it to be 37 years old, 50% don’t.
What is cystic fibrosis?
Cystic fibrosis is an inherited chronic disease that affects the lungs and digestive system of about 30,000 children and adults in the United States (70,000 worldwide). A defective gene and its protein product cause the body to produce unusually thick, sticky mucus that:
- clogs the lungs and leads to life-threatening lung infections; and
- obstructs the pancreas and stops natural enzymes from helping the body break down and absorb food.
In the 1950s, few children with cystic fibrosis lived to attend elementary school. Today, advances in research and medical treatments have further enhanced and extended life for children and adults with CF. Many people with the disease can now expect to live into their 30s, 40s and beyond.
Symptoms of cystic fibrosis
People with CF can have a variety of symptoms, including:
- very salt-tasting skin;
- persistent coughing, at times with phlegm;
- frequent lung infections;
- wheezing or shortness of breath;
- poor growth/weight gain in spite of a good appetite; and
- frequent greasy, bulky stools or difficulty in bowel movements.
- About 1,000 new cases of cystic fibrosis are diagnosed each year.
- More than 70% of patients are diagnosed by age two.
- More than 45% of the CF patient population is age 18 or older.
- The predicted median age of survival for a person with CF is the mid-30s
The Cystic fibrosis foundation
Since 1955, the Cystic Fibrosis Foundation has been the driving force behind the pursuit of a cure. Thanks to the dedication and financial backing of our supporters--patients, families and friends, clinicians, researchers, volunteers, individual donors, corporations and staff, we are making a difference.